US AND CT OF CAROLI DISEASE: REPORT OF TWO CASES
Abstract
Caroli disease is a rare congenital disorder with multiple cystic dilatation of the intrahepatic bile ducts. We report two pediatric patients with cystic dilatation of intrahepatic bile ducts accompanying congenital hepatic fibrosis. CT scans of the liver showed tiny dots with strong contrast enhancement inside dilated intrahepatic bile ducts ("central dot signs"). These dot signs in CT scans corresponded to intraluminal portal veins in sonograms. Ultrasonography and CT scans are very effective noninvasive methods to diagnose this disease.
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